What does the word gastroschisis mean?

1.   ?    Belly cleft
2.   ?    Thickened bowel
3.   ?    Large stomach

Gastroschisis occurs at the site where what normally involutes?

1.   ?    Umbilical artery
2.   ?    Umbilical vein
3.   ?    Vitelline vein
4.   ?    Umbilical vein

Which is more common: gastroschisis or omphalocele?

1.   ?    Gastroschisis
2.   ?    Omphalocele
3.   ?    They are equivalent

What percent of patients with gastroschisis are premature?

1.   ?    10 Percent
2.   ?    25 Percent
3.   ?    40 Percent
4.   ?    65 Percent

What percent of patients with gastroschisis are male?

1.   ?    10 Percent
2.   ?    25 Percent
3.   ?    50 Percent
4.   ?    75 Percent

What percent of patients with gastroschisis have intestinal atresia?

1.   ?    10 Percent
2.   ?    25 Percent
3.   ?    50 Percent
4.   ?    75 Percent

Fluid requirements for an infant with gastroschisis are about how much more than normal?

1.   ?    Not different
2.   ?    1.5 times normal
3.   ?    2 - 3 times normal
4.   ?    4 - 5 times normal

What is the maximum ventilatory pressure which can be tolerated during attempted complete closure of gastroschisis?

1.   ?    25 cm H2O
2.   ?    30 cm H2O
3.   ?    35 cm H2O
4.   ?    45 cm H2O

How often can primary closure be obtained in gastroschisis?

1.   ?    10 Percent
2.   ?    20 Percent
3.   ?    50 Percent
4.   ?    70 Percent

How many calories per day are given parenterally to an infant with gastroschisis?

1.   ?    80 - 100 kcal/kg/day
2.   ?    100 - 120 kcal/kg/day
3.   ?    125 - 130 kcal/kg/day
4.   ?    150 - 200 kcal/kg/day

What is the management of intestinal atresia in gastroschisis?

1.   ?    Initial primary anastomosis
2.   ?    Ileostomy
3.   ?    Drop and wait
4.   ?    Koop stoma

At what stage of fetal development does omphalocele occur?

1.   ?    1st week
2.   ?    2nd week
3.   ?    3rd week
4.   ?    4th week

Omphaloceles are covered by a sac composed of an outer layer of ___ and an inner layer of _____?

1.   ?    Amnion and Wharton's membrane
2.   ?    Amnion and peritoneum
3.   ?    Amnion and chorion
4.   ?    Chorion and amnion

What is the incidence of omphalocele?

1.   ?    1 in 1,000 live births
2.   ?    1 in 5,000 live births
3.   ?    1 in 10,000 live births
4.   ?    1 in 15,000 live births

What is the incidence of associated anomalies in patients with omphalocele?

1.   ?    10 Percent
2.   ?    25 Percent
3.   ?    50 Percent
4.   ?    75 Percent

Beckwith-Wiedemann syndrome is associated with omphalocele. What associated pancreatic anomaly is present?

1.   ?    Absent islet cells
2.   ?    Decreased islet cells
3.   ?    Islet cell hyperplasia
4.   ?    Increased alpha cells

Which is NOT part of pentalogy of Cantrell?

1.   ?    Pericardial defect
2.   ?    Sternal cleft
3.   ?    Omphalocele
4.   ?    Diaphragmatic (posterior) hernia

True or false: the smaller the defect, the better the prognosis for the omphalocele?

1.   ?    True
2.   ?    False

How often is the liver present within the omphalocele sac?

1.   ?    10 Percent
2.   ?    33 Percent
3.   ?    50 Percent
4.   ?    66 Percent

True or false: Meckel's diverticulum is seen with increased frequency in patients with omphalocele?

1.   ?    True
2.   ?    False

What serum marker may be elevated in isolated omphalocele?

1.   ?    HCG
2.   ?    CEA
3.   ?    LDH
4.   ?    AFP

What percent of patients with omphalocele have a ruptured sac?

1.   ?    5 Percent
2.   ?    10 Percent
3.   ?    15 Percent
4.   ?    25 Percent

What topical agent is NOT (including historically) used in very large omphaloceles to treat the sac?

1.   ?    Silver nitrate
2.   ?    Mercurochrome
3.   ?    Alcohol
4.   ?    Phenol

What is the mortality for infants with pentalogy of Cantrell?

1.   ?    10 Percent
2.   ?    25 Percent
3.   ?    50 Percent
4.   ?    75 Percent