What disease is NOT associated with congenital arterial disorders?

1.   ?    Ehler-Danlos
2.   ?    Turner?s syndrome
3.   ?    Scleroderma
4.   ?    Cystinosis

What arterial abnormality is most common in Marfan's syndrome?

1.   ?    Ascending aortic aneurysm
2.   ?    Descending aortic aneurysm
3.   ?    Abdominal aortic aneurysm

What are the most common arterial abnormalities seen in Ehlers-Danlos syndrome?

1.   ?    Peripheral arterial aneurysm
2.   ?    Splenic artery aneurysm
3.   ?    Aortic aneurysm

T or F: The most common pediatric visceral artery aneurysm is hepatic?

1.   ?    True
2.   ?    False

True or false: most arteriovenous malformations are peripheral, localized, and amenable to excision?

1.   ?    True
2.   ?    False

What is the most common location for arteriovenous malformations?

1.   ?    Lower extremity
2.   ?    Upper extremity
3.   ?    Neck
4.   ?    Trunk

What syndrome is associated with microfistulous arteriovenous malformations and limb overgrowth?

1.   ?    Parkes-Weber syndrome
2.   ?    Sturge-Weber syndrome
3.   ?    Klippel-Feil-Trenauny

T or F: isolated macrofistulous arteriovenous malformations of the extremity are often associated with late overgrowth of the limb?

1.   ?    True
2.   ?    False

Although visceral artery aneurysms are exceedingly rare in children, at what size should resection be done?

1.   ?    Greater than 1 cm
2.   ?    Greater than 2 cm
3.   ?    Greater than 4 cm

What is the most common congenital childhood disorder resulting in aneurysm formation?

1.   ?    Kawasaki's disease
2.   ?    Marfan?s syndrome
3.   ?    Ehler-Danlos syndrome
4.   ?    Turner?s syndrome

Which is NOT a sign or symptom of Kawasaki's disease?

1.   ?    Rash
2.   ?    Pedal edema
3.   ?    Arthritis
4.   ?    Conjunctivitis

T or F: Infants with leukemia have increased risk of vascular thrombosis?

1.   ?    True
2.   ?    False

What is the treatment for most children with arterial thromboses of the extANSWERies?

1.   ?    FFP
2.   ?    Coumadin
3.   ?    Heparin
4.   ?    Urokinase

What is the management of aortic thrombosis associated with CHF and extreme HTN?

1.   ?    Thrombectomy
2.   ?    Heparin
3.   ?    Urokinase
4.   ?    All of the above

T or F: Blindness is a complication of Takayasu's disease?

1.   ?    True
2.   ?    False

What is the incidence of surgically correctable hypertension in children between 5 ? 10 yrs old?

1.   ?    10%
2.   ?    25%
3.   ?    About 50%
4.   ?    75%

What is the most common cause of surgically correctable hypertension in children?

1.   ?    Renovascular
2.   ?    Aortic coarctation
3.   ?    Fibromuscular dysplasia
4.   ?    Pheochromocytoma

How often does fibromuscular dysplasia of the renal artery affect both sides?

1.   ?    10%
2.   ?    30%
3.   ?    60%
4.   ?    80%

What is the mean age at diagnosis for fibromuscular dysplasia of the renal arteries?

1.   ?    1 year
2.   ?    6 years
3.   ?    10 years
4.   ?    23 years