How is cystic fibrosis inherited?

1.   ?    Autosomal recessive
2.   ?    Autosomal dominant
3.   ?    Unknown
4.   ?    X-linked recessive

What percentage of children with cystic fibrosis present with intestinal obstruction due to meconium ileus?

1.   ?    5%
2.   ?    15 - 20%
3.   ?    25%
4.   ?    40%

What percent of patients with cystic fibrosis have failure of secretions of pancreatic enzymes into the duodenum?

1.   ?    50%
2.   ?    75%
3.   ?    90%

How long after birth is the obstruction due to meconium ileus usually evident?

1.   ?    24 - 48 hrs
2.   ?    72 hrs
3.   ?    4 - 5 days

How often is there a history of polyhydramnios in patients with meconium ileus?

1.   ?    5%
2.   ?    10%
3.   ?    20%
4.   ?    40%

How does prematurity relate to meconium ileus?

1.   ?    60 - 70% of MI patients are premature
2.   ?    30 - 50% of MI patients are premature
3.   ?    Prematurity is uncommon in MI

Which is NOT one of the typical plain radiographic findings in meconium ileus?

1.   ?    Air-fluid levels
2.   ?    Sop-bubble appearance
3.   ?    Microcolon on BE
4.   ?    Varying size of dilated loops of bowel

T or F: A barium enema should be obtained in patients with suspected complicated meconium ileus?

1.   ?    True
2.   ?    False

In the sweat chloride test, how does pilocarpine work?

1.   ?    Directly stimulates sweat production
2.   ?    Dilates sweat gland ducts
3.   ?    Mediates active sodium transport in sweat glands
4.   ?    Mediates active chloride transport in sweat glands

What percentage of patients with simple meconium ileus can be treated successfully with contrast enemas?

1.   ?    Less than 5%
2.   ?    15 - 25%
3.   ?    30 - 40%
4.   ?    60 - 75%

Which is NOT seen in complicated meconium ileus?

1.   ?    Perforation
2.   ?    Meconium ascites
3.   ?    Intestinal atresia
4.   ?    Intussusception

When does meconium ileus equivalent usually present?

1.   ?    25 - 35 yrs of age
2.   ?    Teenagers / adolescents
3.   ?    Infants / toddlers
4.   ?    Newborns

What percentage of patients with small left colon syndrome have a history of maternal diabetes?

1.   ?    5%
2.   ?    25%
3.   ?    50%
4.   ?    75%

Where do trichobezoars usually occur?

1.   ?    Stomach
2.   ?    Duodenum and jejunum
3.   ?    Ileum
4.   ?    Colon

Where do phytobezoars usually occur?

1.   ?    Stomach
2.   ?    Duodenum and jejunum
3.   ?    Ileum
4.   ?    Colon

What is NOT a medication which can potentially lead to concretions which plug the intestine?

1.   ?    Antacids
2.   ?    Cholestyramine
3.   ?    Kayexelate
4.   ?    Magnesium citrate

What is the most common parasite causing distal intestinal obstruction?

1.   ?    Ascaris
2.   ?    Entameoba histolytica
3.   ?    Echinococcus