Skin

Congenital absence of the scalp is ____ associated with other anomalies?
1. Frequently
2. Rarely
Nevi originate from what cell type?
1. Melanocytes
2. Melanoblasts
3. Junctional cells
T or F: An intradermal nevus usually is seen in adults, but may present in childhood, and is raised and often hairy?
1. True
2. False
Is a blue nevus premalignant?
1. Yes
2. No
True or false: Juvenile melanoma is a highly malignant tumor of childhood and should be treated aggressively?
1. True
2. False
The risk of malignant change in giant and bathing trunk nevi is ____?
1. Less than 5%
2. Less than 10%
3. 35%
4. 50%
Benign, yellow plaque-like skin nodules with cholesterol abnormalities, areas of tissue destruction and foam cells are ___?
1. Spitz nevus
2. Junctional nevus
3. Xanthoma
4. Langerhans cell
Epidermolysis bullosa is associated with a defect in what?
1. Fibroblasts
2. Macrophages
3. Elastic fibers in the skin
4. Collagen cross-linking
Congenital skin bands should be treated by serial Z-plasty maneuvers beginning at ___ months?
1. Birth
2. 3 months
3. 6 months
4. 12 months
What syndrome is associated with skin webbing of the neck?
1. KlinefelterÂ’s syndrome
2. TurnerÂ’s syndrome
3. CruozonÂ’s disease
4. ApertÂ’s syndrome
What syndrome is characterized by generalized hypertrophy and overdevelopment of whole body musculature?
1. XXY - Superman syndrome
2. WerndigÂ’s dystrophy
3. WrestlerÂ’s syndrome
Central hand defects (split lobster claw) or pincer hand results in a totally useless hand and early amputation or reconstruction is recommended?
1. True
2. False
Which is NOT true of MadelungÂ’s deformity?
1. Radial epiphyseal abnormalities
2. Dorsal prominence of distal ulna
3. 90% bilateral
4. Adolescent females most commonly affected group
What is the most common site for dermoid cysts?
1. Supraorbital
2. Clavicular head
3. Neck
4. Hand
In neurofibromatosis, the number of cafÃ©-au-lait spots remains stable throughout life: True or false?
1. True
2. False
What congenital nevus is associated with von Recklinghausen's disease?
1. Spitz Nevus
2. Melanoma congenita
3. Giant bathing trunk nevus
Von Recklinghausen's neurofibromatosis is transmitted by what type of genetic disorder?
1. Autosomal recessive
2. Autosomal dominant
3. X Â– linked recessive
In VRD, where do the nerve tumors usually arise from?
1. Schwann cells from the neural crest
2. Dendrites
3. Histiocystic APUD derivatives
What percent of children with VRD will have signs of the disease at birth?
1. 10%
2. 20%
3. 45%
4. 75%
Are there usually neurological symptoms from the neurofibromas in VRD?
1. Yes
2. No
If a boy and a girl both have VRD, who has the greater risk of sarcomatous degeneration?
1. Boys greater than Girls
2. Girls greater than Boys
What are the 2 forms of VRD?
1. Diffuse and Localized
2. Central and Peripheral
3. Dominant and Recessive
T or F: Bony abnormalities in VRD may occur in the absence of any neurofibromatous disease?
1. True
2. False
Which of the clinical forms of von Recklinghausen's disease tends to involve the scalp?
1. Elephantiasis nervorum
2. Neurofibrosarcoma
3. Central neurofibromatosis
What is the rate of malignancy in mediastinal and thoracic neurofibromas?
1. 1 Â– 5%
2. 5 - 40%
3. 40 Â– 60%
4. Greater than 75%
Optic gliomas and acoustic neuromas are NOT associated with VRD: T or F?
1. True
2. False
Is infantile myofibromatosis malignant?
1. Yes
2. No
What substance is increased in a ganglion cyst?
1. Ascorbic acid
2. Collagenase
3. Integrin
4. Hyaluronic acid
Is giant-cell synovioma malignant?
1. Yes
2. No
Which is NOT a common site for malignant synovioma?
1. Knees
2. Hand
3. Foot
4. Face

Skin

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